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Table 1 Summarized data from primary ureteric SmCCa reported in the literature

From: Primary small cell carcinoma of the ureter with associated hyponatremia and rapid progression to bladder involvement: a case report

Authors

Age/Sex

Symptoms

Location

Staging

Pathology

Treatment

Follow up (months, status)

Present case

77 F

Haematuria

Right

T3N0M0

AE/AE3, Syn, CD56

NACT + RT

20 months, AWNR

Zhao et al

70 F

Flank pain

Left

T3N0M0

CgA, CD56, Syn, NsE

NU

9 months, DOD

Akshay et al

55 F

Flank pain, haematuria

Right

T3N2M0

Syn

NACT + NU

3 months, AWNR

Farci et al

79 F

Flank pain, haematuria

Right

T3N1M0

CgA, Syn, CD56

NACT (1cycle), SU

5 months, DOD

Sato et al

63 M

Flank pain

Right

T3N0M0

AE1/AE3, Syn

NACT + NU

6 months, AWNR

Jang et al

59 M

Haematuria

Left

T2N0M0

NsE, CD56, Syn, CgA

NACT + RT

10 months, AWNR

Ahsaini et al

54 M

Haematuria

Left

T2N0M0

NsE, CgA, Syn

NACT + NU

24 months, AWNR

Kozyrakis et al

78 M

Haematuria

Right

T3N0M0

CD56, Syn, CgA

NU

6 months, DOD

Kho et al

77 M

Flank pain

Left

T3N0M0

CgA

NACT + NU

4 months, DOD

Osaka et al

70 M

Flank pain

Left

T3N0M0

CD56, Syn

NACT + NU

38 months, AWNR

Rupert et al

72 M

Asymptomatic

Right

T3N0M0

CD56, Syn, CgA

NU + Chemo

22 months, AWR

Hensley et al

67 F

Flank pain, haematuria

Left

T4N1M0

Syn, CgA

NU + Chemo + RT

7 months, DOD

Ouzzane et al

66 F

Flank pain

Left

T3N0M0

CD56, CgA, Syn

Nil

5 months, DOD

Yang et al

70 F

Flank pain

Left

T3N0M0

CgA

NU

9 months, AWR

  1. Only cases written in English and of proven primary SmCCa without synchronous neoplasms elsewhere in urinary tract or in different organs are reviewed
  2. AWNR alive with no evidence of recurrence, AWR alive with recurrence, DOD dead of disease, NU nephroureterectomy, SU segmental ureterectomy, M male, F female, NsE neuron specific enolase, CgA Chromogranin A, Syn synaptophysin