Authors
|
Age/Sex
|
Symptoms
|
Location
|
Staging
|
Pathology
|
Treatment
|
Follow up (months, status)
|
---|
Present case
|
77 F
|
Haematuria
|
Right
|
T3N0M0
|
AE/AE3, Syn, CD56
|
NACT + RT
|
20 months, AWNR
|
Zhao et al
|
70 F
|
Flank pain
|
Left
|
T3N0M0
|
CgA, CD56, Syn, NsE
|
NU
|
9 months, DOD
|
Akshay et al
|
55 F
|
Flank pain, haematuria
|
Right
|
T3N2M0
|
Syn
|
NACT + NU
|
3 months, AWNR
|
Farci et al
|
79 F
|
Flank pain, haematuria
|
Right
|
T3N1M0
|
CgA, Syn, CD56
|
NACT (1cycle), SU
|
5 months, DOD
|
Sato et al
|
63 M
|
Flank pain
|
Right
|
T3N0M0
|
AE1/AE3, Syn
|
NACT + NU
|
6 months, AWNR
|
Jang et al
|
59 M
|
Haematuria
|
Left
|
T2N0M0
|
NsE, CD56, Syn, CgA
|
NACT + RT
|
10 months, AWNR
|
Ahsaini et al
|
54 M
|
Haematuria
|
Left
|
T2N0M0
|
NsE, CgA, Syn
|
NACT + NU
|
24 months, AWNR
|
Kozyrakis et al
|
78 M
|
Haematuria
|
Right
|
T3N0M0
|
CD56, Syn, CgA
|
NU
|
6 months, DOD
|
Kho et al
|
77 M
|
Flank pain
|
Left
|
T3N0M0
|
CgA
|
NACT + NU
|
4 months, DOD
|
Osaka et al
|
70 M
|
Flank pain
|
Left
|
T3N0M0
|
CD56, Syn
|
NACT + NU
|
38 months, AWNR
|
Rupert et al
|
72 M
|
Asymptomatic
|
Right
|
T3N0M0
|
CD56, Syn, CgA
|
NU + Chemo
|
22 months, AWR
|
Hensley et al
|
67 F
|
Flank pain, haematuria
|
Left
|
T4N1M0
|
Syn, CgA
|
NU + Chemo + RT
|
7 months, DOD
|
Ouzzane et al
|
66 F
|
Flank pain
|
Left
|
T3N0M0
|
CD56, CgA, Syn
|
Nil
|
5 months, DOD
|
Yang et al
|
70 F
|
Flank pain
|
Left
|
T3N0M0
|
CgA
|
NU
|
9 months, AWR
|
- Only cases written in English and of proven primary SmCCa without synchronous neoplasms elsewhere in urinary tract or in different organs are reviewed
- AWNR alive with no evidence of recurrence, AWR alive with recurrence, DOD dead of disease, NU nephroureterectomy, SU segmental ureterectomy, M male, F female, NsE neuron specific enolase, CgA Chromogranin A, Syn synaptophysin